Moyamoya disease
Suzuki staging system for Moyamoya
| Stage | Finding |
|---|---|
| 1 | Stenosis of suprasellar ICA, usually bilateral |
| 2 | Development of moyamoya vessels at base of brain. ACA, MCA, & PCA dilated |
| 3 | Increasing ICA stenosis & prominence of moyamoya vessels (most cases diagnosed at this stage). Maximal basal moyamoya |
| 4 | Entire circle of Willis and PCAs occluded, extracranial collaterals start to appear, moyamoya vessels begin to diminish |
| 5 | Further progression of stage 4 with intensification of ECA collaterals & reduction of moyamoya associated vessels |
| 6 | Total occlusion of ICA & major cerebral arteries and complete absence of moyamoya vessels |