Von Hippel-Lindau disease: Difference between revisions
Jump to navigation
Jump to search
No edit summary |
|||
| Line 7: | Line 7: | ||
</tr> | </tr> | ||
<tr | <tr> | ||
<td rowspan="4">Hemangioblastomas</td> | <td rowspan="4">[[Hemangioblastoma|Hemangioblastomas]]</td> | ||
<td | <td>Cerebellum (solid or cystic)</td> | ||
<td>80%</td> | <td>80%</td> | ||
</tr> | </tr> | ||
<tr> | <tr> | ||
<td> | <td>Retina</td> | ||
<td>41–59%</td> | <td>41–59%</td> | ||
</tr> | </tr> | ||
<tr> | <tr> | ||
<td> | <td>Brainstem</td> | ||
<td>10–25%</td> | <td>10–25%</td> | ||
</tr> | </tr> | ||
<tr> | <tr> | ||
<td> | <td>Spinal cord</td> | ||
<td>10–50%</td> | <td>10–50%</td> | ||
</tr> | </tr> | ||
Latest revision as of 01:58, 5 March 2024
Associations with von Hippel-Lindau disease
| Common Lesions | Frequency in VHL | |
|---|---|---|
| Hemangioblastomas | Cerebellum (solid or cystic) | 80% |
| Retina | 41–59% | |
| Brainstem | 10–25% | |
| Spinal cord | 10–50% | |
| Pancreatic tumors or cysts | 22–80% | |
| Renal clear cell carcinoma & cysts | 14–60% | |
| Polycythemia | 9–20% of intracranial hemangioblastomas | |
| Rare Lesions (pertinent to nervous system) | ||
| Supratentorial hemangioblastoma | 3–6% | |
| Cystadenomas of the broad ligament | 10% of females | |
| Papillary cystadenomas of the epididymis | 25–60% of males | |
| Endolymphatic sac tumors | 10–15% | |
| Adrenal medullary pheochromocytoma (tends to be bilateral) | 7–24% | |