Von Hippel-Lindau disease: Difference between revisions

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= Associations with von Hippel-Lindau disease =
<table class="wikitable" width="100%">
 
  <tr id="yui_3_17_2_1_1709596495879_122">
    <th colspan="2" id="yui_3_17_2_1_1709596495879_121">Common Lesions</th>
    <th>Frequency in VHL</th>
  </tr>
 
  <tr>
    <td rowspan="4">[[Hemangioblastoma|Hemangioblastomas]]</td>
    <td>Cerebellum (solid or cystic)</td>
    <td>80%</td>
  </tr>
  <tr>
    <td>Retina</td>
    <td>41–59%</td>
  </tr>
  <tr>
    <td>Brainstem</td>
    <td>10–25%</td>
  </tr>
  <tr>
    <td>Spinal cord</td>
    <td>10–50%</td>
  </tr>
  <tr>
    <td colspan="2">Pancreatic tumors or cysts</td>
    <td>22–80%</td>
  </tr>
  <tr>
    <td colspan="2">Renal clear cell carcinoma &amp; cysts</td>
    <td>14–60%</td>
  </tr>
  <tr>
    <td colspan="2">Polycythemia</td>
    <td>9–20% of intracranial hemangioblastomas</td>
  </tr>
  <tr>
    <td colspan="3">Rare Lesions (pertinent to nervous system)</td>
  </tr>
  <tr>
    <td colspan="2">Supratentorial hemangioblastoma</td>
    <td>3–6%</td>
  </tr>
  <tr>
    <td colspan="2">Cystadenomas of the broad ligament</td>
    <td>10% of females</td>
  </tr>
  <tr>
    <td colspan="2">Papillary cystadenomas of the epididymis</td>
    <td>25–60% of males</td>
  </tr>
  <tr>
    <td colspan="2">Endolymphatic sac tumors</td>
    <td>10–15%</td>
  </tr>
  <tr>
    <td colspan="2">Adrenal medullary pheochromocytoma (tends to be bilateral)</td>
    <td>7–24%</td>
  </tr>
 
</table>
 
[[Category:Neuro-Oncology]]
[[Category:Neuro-Oncology]]
[[Category:Genetic Syndromes of Brain Tumors]]
[[Category:Genetic Syndromes of Brain Tumors]]

Latest revision as of 01:58, 5 March 2024

Associations with von Hippel-Lindau disease

Common Lesions Frequency in VHL
Hemangioblastomas Cerebellum (solid or cystic) 80%
Retina 41–59%
Brainstem 10–25%
Spinal cord 10–50%
Pancreatic tumors or cysts 22–80%
Renal clear cell carcinoma & cysts 14–60%
Polycythemia 9–20% of intracranial hemangioblastomas
Rare Lesions (pertinent to nervous system)
Supratentorial hemangioblastoma 3–6%
Cystadenomas of the broad ligament 10% of females
Papillary cystadenomas of the epididymis 25–60% of males
Endolymphatic sac tumors 10–15%
Adrenal medullary pheochromocytoma (tends to be bilateral) 7–24%